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Persistent fifth arch anomalies – broadening the spectrum to include a variation of double aortic arch vascular ring

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Abstract

Fifth arch anomalies are rare and complex and frequently misdiagnosed or mistaken for other entities. We report a double arch vascular ring that is thought to consist of right fourth arch and left fifth arch components, a previously undescribed persistent fifth arch variant. The currently recognized spectrum and classification of fifth arch vascular anomalies are expanded along with illustrative images to justify the proposed changes. Reviewing and expanding the classification of fifth arch anomalies to include a double arch ring variant will promote recognition, correct diagnosis and appropriate management of these anomalies.

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Authors and Affiliations

  1. Department of Radiology, Stanford Children’s Hospital and Stanford University, 725 Welch Road, Stanford, CA, 94305, USA

    Beverley Newman & Frandics Chan

  2. Department of Medical Imaging, University of Toronto, Toronto, ON, Canada

    Kate Hanneman

Authors
  1. Beverley Newman
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  2. Kate Hanneman
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  3. Frandics Chan
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Correspondence to Beverley Newman.

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Newman, B., Hanneman, K. & Chan, F. Persistent fifth arch anomalies – broadening the spectrum to include a variation of double aortic arch vascular ring. Pediatr Radiol 46, 1866–1872 (2016). https://doi.org/10.1007/s00247-016-3693-9

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  • DOI: https://doi.org/10.1007/s00247-016-3693-9

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