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Anomalous origin of the left coronary artery from the pulmonary artery in children: diagnostic use of multidetector computed tomography

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Abstract

Background

Anomalous origin of the left coronary artery from the pulmonary artery is a rare congenital anomaly. It is important to demonstrate the anomalous origin of the left coronary artery and its course before surgery.

Objective

To explore the clinical diagnostic use of multidetector CT coronary angiography in detecting anomalous origin of the left coronary artery from the pulmonary artery in children.

Materials and methods

Nine children (2 boys, 7 girls) ages 2 months to 9 years with surgically confirmed anomalous origin of the left coronary artery from the pulmonary artery were studied. Clinical data, transthoracic echocardiography and CT coronary angiography images were retrospectively analyzed.

Results

Transthoracic echocardiography correctly diagnosed anomalous origin of the left coronary artery from the pulmonary artery in 7 of 9 patients (95% CI: 40–97%). CT coronary angiography revealed the anomalous origin of the left coronary artery in all children (95% CI: 66–100%). In a 4-year-old girl and a 9-year-old girl, CT coronary angiography showed dilation of the right coronary artery and collateral circulation between the right and the left coronary arteries.

Conclusion

CT coronary angiography is a useful method to show the anomalous origin of the coronary artery in children with anomalous origin of the left coronary artery from the pulmonary artery, especially for patients in whom origin of the left coronary artery cannot be detected by transthoracic echocardiography.

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Correspondence to Xihong Hu.

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Shen, Q., Yao, Q. & Hu, X. Anomalous origin of the left coronary artery from the pulmonary artery in children: diagnostic use of multidetector computed tomography. Pediatr Radiol 46, 1392–1398 (2016). https://doi.org/10.1007/s00247-016-3635-6

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  • DOI: https://doi.org/10.1007/s00247-016-3635-6

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