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Bladder exstrophy: current management and postoperative imaging

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Abstract

Bladder exstrophy is a rare malformation characterized by an infra-umbilical abdominal wall defect, incomplete closure of the bladder with mucosa continuous with the abdominal wall, epispadias, and alterations in the pelvic bones and muscles. It is part of the exstrophy–epispadias complex, with cloacal exstrophy on the severe and epispadias on the mild ends of the spectrum. Bladder exstrophy is the most common of these entities and is more common in boys. The goal of this paper is to describe common methods of repair and to provide an imaging review of the postoperative appearances.

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Authors and Affiliations

  1. Department of Radiology, Boston Children’s Hospital, 300 Longwood Ave., Boston, MA, 02115, USA

    Ketsia Pierre & Jeanne S. Chow

  2. Department of Urology, Boston Children’s Hospital, Boston, MA, USA

    Joseph Borer & Jeanne S. Chow

  3. Department of Pediatric Radiology, University of California, San Francisco, San Francisco, CA, USA

    Andrew Phelps

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  1. Ketsia Pierre
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  2. Joseph Borer
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  3. Andrew Phelps
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  4. Jeanne S. Chow
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Correspondence to Ketsia Pierre.

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Pierre, K., Borer, J., Phelps, A. et al. Bladder exstrophy: current management and postoperative imaging. Pediatr Radiol 44, 768–786 (2014). https://doi.org/10.1007/s00247-014-2892-5

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  • DOI: https://doi.org/10.1007/s00247-014-2892-5

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