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Uterus didelphys, hemihydrocolpos and empty ipsilateral lumbar fossa in a newborn girl: involuted dysplastic kidney rather than renal agenesis

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Abstract

We report a case of Herlyn-Werner-Wunderlich syndrome diagnosed in the neonatal period. US revealed the classic association of a uterus didelphys with blind hemivagina and no ipsilateral kidney. The diagnosis was established by postnatal US and confirmed by MRI. Differential diagnoses are discussed. A trans-hymeneal resection of the vaginal septum was performed at 1 month of age. Intra operative endoscopy revealed no left hemitrigone but showed an atretic orifice in the ipsilateral blind hemivagina, probably corresponding to the insertion of an ectopic ureter. Follow-up was unremarkable.

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Authors and Affiliations

  1. Pediatric and Foetal Imaging Service, Department of Radiology, CHU Charles Nicolle, Rouen University Hospital, 1 rue de Germont, 76031, Rouen Cedex, France

    Pierre-Hugues Vivier, Marie Brasseur-Daudruy, Cécile Cellier, Patrick Le Dosseur & Jean-Nicolas Dacher

  2. Department of Pediatric Surgery, University Hospital, 1 rue de Germont, 76031, Rouen Cedex, France

    Agnès Liard & Marion Beurdeley

Authors
  1. Pierre-Hugues Vivier
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  2. Agnès Liard
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  3. Marion Beurdeley
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  4. Marie Brasseur-Daudruy
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  5. Cécile Cellier
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  6. Patrick Le Dosseur
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  7. Jean-Nicolas Dacher
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Correspondence to Pierre-Hugues Vivier.

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Vivier, PH., Liard, A., Beurdeley, M. et al. Uterus didelphys, hemihydrocolpos and empty ipsilateral lumbar fossa in a newborn girl: involuted dysplastic kidney rather than renal agenesis. Pediatr Radiol 41, 1205–1207 (2011). https://doi.org/10.1007/s00247-011-2046-y

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  • DOI: https://doi.org/10.1007/s00247-011-2046-y

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