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An unusual presentation of malignant hepatic epithelioid haemangioendothelioma with left pleural and pulmonary localization

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Abstract

Hepatic epithelioid haemangioendothelioma (HEHE) is extremely rare in children. We present an adolescent who presented with a scoliosis due to left thoracic pain. Multifocal HEHE was incidentally found during CT scan of the thorax, and confirmed with a multiphase CT scan of the abdomen, biopsy and immunochemistry. Left pleural and pulmonary involvement was suspected and later confirmed with biopsy and histopathological examination. The patient died 1 year after diagnosis. To the best of our knowledge, scoliosis has not previously been reported as the first symptom of EHE.

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Authors and Affiliations

  1. Department of Radiology, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IsMeTT), Via Ernesto Tricomi 1, 90127, Palermo, Italy

    Settimo Caruso, Roberto Miraglia, Luigi Maruzzelli & Angelo Luca

  2. Department of Transplantation Surgery, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IsMeTT), Palermo, Italy

    Marco Spada & Bruno Gridelli

  3. Department of Medicine, Pneumology, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IsMeTT), Palermo, Italy

    Patrizio Vitulo

  4. Department of Pathology, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IsMeTT), Palermo, Italy

    Marta Ida Minervini

Authors
  1. Settimo Caruso
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  2. Roberto Miraglia
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  3. Luigi Maruzzelli
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  4. Marco Spada
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  5. Patrizio Vitulo
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  6. Marta Ida Minervini
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  7. Angelo Luca
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  8. Bruno Gridelli
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Correspondence to Settimo Caruso.

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Caruso, S., Miraglia, R., Maruzzelli, L. et al. An unusual presentation of malignant hepatic epithelioid haemangioendothelioma with left pleural and pulmonary localization. Pediatr Radiol 38, 1027–1030 (2008). https://doi.org/10.1007/s00247-008-0915-9

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  • DOI: https://doi.org/10.1007/s00247-008-0915-9

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