Abstract
Background
Because of the rarity of right aortic arch coarctation there are few reports of large groups of patients.
Objective
To characterize the frequency and type of right aortic arch coarctation in a large group of pediatric patients.
Materials and methods
From June 1997 through May 2007, 11,276 consecutive children with congenital heart disease underwent multidetector CT (MDCT), MRI or angiocardiography examination. All children with a right aortic arch or coarctation were reviewed.
Results
Right aortic arch coarctation was found in 11 children representing 0.1% of the total group of 11,276 children, 1.7% of 658 children with native coarctations and 2.3% of 473 children with a right aortic arch. Among the 11 patients, 6 had long-segment narrowing and 7 had an aberrant left subclavian artery.
Conclusion
MDCT, MRI and angiocardiography are reliable imaging techniques for the diagnosis of right aortic arch and coarctation. Our findings showed that the pattern of right aortic arch coarctation was different from that of left aortic arch coarctation, suggesting that they are different etiological entities. The pivotal role possibly played by flow dynamics in the development of right aortic arch coarctation is discussed.
Similar content being viewed by others
References
Gil-Jaurena JM, Murtra M, Gonçalves A et al (2002) Aortic coarctation, vascular ring, and right aortic arch with aberrant subclavian artery. Ann Thorac Surg 73:1640–1642
Delgado C, Baruren F (1998) Coarctation of the aorta with right aortic arch and isolation of the left innominate artery: a surgical challenge in a patient without collateral posterior brain circulation. J Thorac Cardiovasc Surg 116:657–659
Ismat FA, Weinberg PM, Rychik J et al (2006) Right aortic arch and coarctation: a rare association. Congenit Heart Dis 1:217–223
Ming Z, Yumin Z, Yuhua L et al (2006) Diagnosis of congenital obstructive aortic arch anomalies in Chinese children by contrast-enhanced magnetic resonance angiography. J Cardiovasc Magn Reson 8:747–753
Caceres M, Daggett C, Lutterman J et al (2006) Right aortic coarctation and ventricular septal defect: an unusual cause of tracheal compression in infancy. Congenit Heart Dis 1:175–179
Ad N, Vidne BA (1999) Coarctation of the aorta with right aortic arch: surgical technique and new classification. Ann Thorac Surg 67:1125–1129
McElhinney DB, Tworetzky W, Hanley FL et al (1999) Congenital obstructive lesions of the right aortic arch. Ann Thorac Surg 67:1194–1202
Freedom RM, Mawson JB, Yoo S-J et al (eds) (1997) Congenital heart disease. Textbook of angiocardiography. Futura, New York
Craatz S, Künzel E, Spanel-Borowski K (2003) Right-sided aortic arch and tetralogy of Fallot in humans – a morphological study of 10 cases. Cardiovasc Pathol 12:226–232
McElhinney DB, Clark BJ, Weinberg PM et al (2001) Association of chromosome 22q11 deletion with isolated anomalies of aortic arch laterality and branching. J Am Coll Cardiol 37:2114–2119
Rey C, Coeurderoy A, Dupuis C (1984) Coarctation of the aorta and Fallot’s tetralogy. Apropos of 2 cases. Arch Mal Coeur Vaiss 77:526–533
Bein S, Saba Z, Patel H et al (2006) Coarctation of the aorta in the right aortic arch with left aberrant innominate artery. Pediatr Cardiol 27:621–623
Sakamoto Y, Miyazawa S, Suzuki K et al (1992) Right aortic arch with mirror-image branching and coarctation of the aorta – a case report. Nippon Kyobu Geka Gakkai Zasshi 40:1001–1005
Isomatsu Y, Takanashi Y, Terada M et al (2004) Persistent fifth aortic arch and fourth arch interruption in a 28-year-old woman. Pediatr Cardiol 25:696–698
Donnelly LF, Fleck RJ, Pacham P et al (2002) Aberrant subclavian arteries: cross-sectional imaging findings in infants and children referred for evaluation of extrinsic airway compression. AJR 178:1269–1274
Cina CS, Althani H, Pasenau J et al (2004) Kommerell’s diverticulum and right-sided aortic arch: a cohort study and review of the literature. J Vasc Surg 39:131–139
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Ming, Z., Aimin, S. Right aortic arch with coarctation in Chinese children. Pediatr Radiol 38, 511–517 (2008). https://doi.org/10.1007/s00247-008-0756-6
Received:
Revised:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00247-008-0756-6