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Diagnosis of Chiari III malformation by second trimester fetal MRI with postnatal MRI and CT correlation

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Abstract

We report a case of Chiari III malformation diagnosed by fetal MRI. Ultrasound (US) performed at a gestational age of 18 weeks demonstrated a posterior skull base cyst. Repeat US at 19 weeks demonstrated neural tissue in the cyst, consistent with an encephalocele. MR imaging at 23 weeks confirmed the presence of an occipital encephalocele, demonstrated additional bony defect in the upper cervical spine, and identified abnormal morphology and position of the brainstem consistent with the diagnosis of Chiari III. Postnatal MRI and CT confirmed the fetal MRI findings and demonstrate the utility of fetal MRI in the early evaluation of songraphically detected posterior fossa abnormalities.

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References

  1. Chiari H (1891) Uber Verrandergungen des Kleinhims infolge von Hydrocephlic des Grosshims. Dtsch Med Wochenschr 1891, pp 1172–1175

    Google Scholar 

  2. Castillo M, Quencer RM, Dominquez R (1992) Chiari III malformation: Imaging features. AJNR 13:107–113

    PubMed  CAS  Google Scholar 

  3. Cama A, Tortori-Donati P, Piatelli GL et al (1995) Chiari complex in children-neuroradiological diagnosis, neurosurgical treatment and proposal of a new classification (312 cases). Eur J Pediatr Surg 5 (Suppl 1):35–38

    Article  PubMed  Google Scholar 

  4. Levine D, Barnes PD, Edelman RR (1999) Obstetric MR imaging. Radiology 211:609–617

    PubMed  CAS  Google Scholar 

  5. Glenn OA, Barkovich J (2006) Magnetic resonance imaging of the fetal brain and spine: an increasingly important tool in prenatal diagnosis: part 2. AJNR 27:1807–1814

    PubMed  CAS  Google Scholar 

  6. Cakirer S (2003) Chiari III malformation varieties of MRI appearances in two patients. Clin Imaging 27:1–4

    Article  PubMed  CAS  Google Scholar 

  7. Lee R, Tai KS, Cheng PW et al (2002) Chiari III malformation: antenatal MRI diagnosis. Clin Radiol 57:759–767

    Article  PubMed  CAS  Google Scholar 

  8. Sener RN (1995) Cerebellar agenesis versus vanishing cerebellum in Chiari II malformation. Comput Med Imaging Graph 19:491–494

    Article  PubMed  CAS  Google Scholar 

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Authors and Affiliations

  1. Department of Radiology, University of California, San Francisco, San Francisco, CA, USA

    Alice B. Smith & Orit A. Glenn

  2. Department of Neurosurgery, University of California, San Francisco, San Francisco, CA, USA

    Nalin Gupta

  3. Department of Perinatology, California Pacific Medical Center, San Francisco, CA, USA

    Carl Otto

Authors
  1. Alice B. Smith
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  2. Nalin Gupta
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  3. Carl Otto
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  4. Orit A. Glenn
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Corresponding author

Correspondence to Alice B. Smith.

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Smith, A.B., Gupta, N., Otto, C. et al. Diagnosis of Chiari III malformation by second trimester fetal MRI with postnatal MRI and CT correlation. Pediatr Radiol 37, 1035–1038 (2007). https://doi.org/10.1007/s00247-007-0549-3

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  • DOI: https://doi.org/10.1007/s00247-007-0549-3

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