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Pediatric Radiology

, Volume 36, Issue 11, pp 1215–1218 | Cite as

Aneurysm of the ductus arteriosus in a patient with Larsen syndrome

  • Bo-Kyung Je
  • So-Young Yoo
  • Whal Lee
  • Woo Sun Kim
  • In-One KimEmail author
Case Report

Abstract

Larsen syndrome is characterized by multiple congenital joint dislocations and a characteristic flattened facial appearance. The aetiology is unknown, but the syndrome is considered a probable connective tissue disorder and the cardiovascular manifestations are similar to those of Marfan syndrome. We describe an 8-year-old girl with the characteristic features of Larsen syndrome who was also affected by a saccular aneurysm of the descending aorta, just distal to the left subclavian artery. We present the radiological findings and review the literature.

Keywords

Larsen syndrome Thoracic aortic aneurysm CT Child 

References

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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Bo-Kyung Je
    • 1
  • So-Young Yoo
    • 2
  • Whal Lee
    • 3
  • Woo Sun Kim
    • 3
  • In-One Kim
    • 3
    Email author
  1. 1.Department of Diagnostic RadiologyKorea University Ansan HospitalDanwon-gu, Ansan-siSouth Korea
  2. 2.Department of Radiology, Samsung Medical CenterSungkyunkwan University School of MedicineSeoulSouth Korea
  3. 3.Department of RadiologySeoul National University College of MedicineSeoulKorea

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