Pediatric Radiology

, Volume 36, Issue 11, pp 1215–1218 | Cite as

Aneurysm of the ductus arteriosus in a patient with Larsen syndrome

  • Bo-Kyung Je
  • So-Young Yoo
  • Whal Lee
  • Woo Sun Kim
  • In-One KimEmail author
Case Report


Larsen syndrome is characterized by multiple congenital joint dislocations and a characteristic flattened facial appearance. The aetiology is unknown, but the syndrome is considered a probable connective tissue disorder and the cardiovascular manifestations are similar to those of Marfan syndrome. We describe an 8-year-old girl with the characteristic features of Larsen syndrome who was also affected by a saccular aneurysm of the descending aorta, just distal to the left subclavian artery. We present the radiological findings and review the literature.


Larsen syndrome Thoracic aortic aneurysm CT Child 


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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Bo-Kyung Je
    • 1
  • So-Young Yoo
    • 2
  • Whal Lee
    • 3
  • Woo Sun Kim
    • 3
  • In-One Kim
    • 3
    Email author
  1. 1.Department of Diagnostic RadiologyKorea University Ansan HospitalDanwon-gu, Ansan-siSouth Korea
  2. 2.Department of Radiology, Samsung Medical CenterSungkyunkwan University School of MedicineSeoulSouth Korea
  3. 3.Department of RadiologySeoul National University College of MedicineSeoulKorea

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