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Pediatric Radiology

, Volume 36, Issue 11, pp 1200–1203 | Cite as

Optic pathway glioma associated with orbital rhabdomyosarcoma and bilateral optic nerve sheath dural ectasia in a child with neurofibromatosis-1

  • Ioannis Nikas
  • Maria TheofanopoulouEmail author
  • Penelope Lampropoulou
  • Apostolos Pourtsidis
  • Christiana Hadjigeorgi
  • Helen Kosmidis
Case Report

Abstract

Neurofibromatosis-1 (NF-1) is a multisystem disorder presenting with a variety of clinical and imaging manifestations. Neural and non-neural tumours, and unusual benign miscellaneous conditions, separately or combined, are encountered in variable locations. We present a 2½-year-old boy with NF-1 who demonstrated coexisting optic pathway glioma with involvement of the chiasm and optic nerve, orbital alveolar rhabdomyosarcoma and bilateral optic nerve sheath dural ectasia.

Keywords

Neurofibromatosis-1 Optic pathway glioma Orbital rhabdomyosarcoma Dural ectasia of the optic nerve sheath Child 

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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Ioannis Nikas
    • 1
  • Maria Theofanopoulou
    • 1
    Email author
  • Penelope Lampropoulou
    • 1
  • Apostolos Pourtsidis
    • 2
  • Christiana Hadjigeorgi
    • 1
  • Helen Kosmidis
    • 2
  1. 1.Imaging DepartmentAghia Sophia Children’s HospitalAthensGreece
  2. 2.Department of OncologyChildren’s Hospital, A. KyriakouAthensGreece

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