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CT of tracheal agenesis

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Abstract

Background

Tracheal agenesis is a rare and usually lethal anomaly. In the past, opaque contrast medium was injected via the esophagus to demonstrate the anatomy.

Objective

To demonstrate the utility of helical and multidetector CT in delineating the aberrant anatomy in newborns with tracheal agenesis.

Materials and methods

Four newborns with tracheal agenesis were identified from three institutions. Imaging studies and medical records were reviewed. Each child was imaged with chest radiography. One child was imaged on a single-detector helical CT scanner and the other three on multidetector scanners.

Results

Helical and multidetector CT with 2D and 3D reconstructions clearly delineated the aberrant tracheobronchial and esophageal anatomy in each infant. Minimum intensity projection reformatted CT images were particularly helpful. One infant each had type I and type II tracheal agenesis. Two infants had type III tracheal agenesis. All four infants died.

Conclusion

CT is a useful tool for delineating the aberrant anatomy of newborns with tracheal agenesis and thus helps in making rational clinical decisions.

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Authors and Affiliations

  1. Section of Pediatric Radiology, C. S. Mott Children’s Hospital, Department of Radiology, University of Michigan Health System, 1500 East Medical Center Dr, Ann Arbor, MI, 48103-0252, USA

    Peter J. Strouse & Ramiro J. Hernandez

  2. Department of Pediatric Radiology, Children’s Hospital of Pittsburgh, University of Pittsburgh, Pittsburgh, PA, USA

    Beverley Newman

  3. Departments of Radiology and Pediatrics, Children’s Hospital Of Buffalo, Buffalo, NY, USA

    Ehsan Afshani

  4. Division of Neonatology, University Pediatrics Associates, Women’s and Children’s Hospital of Buffalo, Buffalo, NY, USA

    Mahesh Bommaraju

Authors
  1. Peter J. Strouse
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  2. Beverley Newman
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  3. Ramiro J. Hernandez
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  4. Ehsan Afshani
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  5. Mahesh Bommaraju
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Corresponding author

Correspondence to Peter J. Strouse.

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Strouse, P.J., Newman, B., Hernandez, R.J. et al. CT of tracheal agenesis. Pediatr Radiol 36, 920–926 (2006). https://doi.org/10.1007/s00247-006-0231-1

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  • DOI: https://doi.org/10.1007/s00247-006-0231-1

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