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Coexistence of pleomorphic xanthoastrocytoma with Sturge-Weber syndrome: MRI features

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Abstract

Pleomorphic xanthoastrocytoma is a rare, cortically based, partially cystic astroglial tumour with a strongly enhancing solid mural nodule. We report an 11-year-old boy with a pleomorphic xanthoastrocytoma in the contralateral hemisphere to that affected by Sturge-Weber syndrome. This unique case supports the association between Sturge-Weber syndrome and astrocytomas. Patients with Sturge-Weber syndrome who experience unexpected neurological symptoms should be evaluated with MRI.

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Authors and Affiliations

  1. Department of Radiology, Diyarbakir Military Hospital, Diyarbakir, 21100, Turkey

    Ozgur Kilickesmez, Hatice Tuba Sanal & Erhan Kocamaz

  2. Department of Pathology, GATA Haydarpasa Training Hospital, Istanbul, Turkey

    Aptullah Haholu

Authors
  1. Ozgur Kilickesmez
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  2. Hatice Tuba Sanal
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  3. Aptullah Haholu
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  4. Erhan Kocamaz
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Correspondence to Ozgur Kilickesmez.

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Kilickesmez, O., Sanal, H.T., Haholu, A. et al. Coexistence of pleomorphic xanthoastrocytoma with Sturge-Weber syndrome: MRI features. Pediatr Radiol 35, 910–913 (2005). https://doi.org/10.1007/s00247-005-1480-0

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  • DOI: https://doi.org/10.1007/s00247-005-1480-0

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