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Congenital short-gut syndrome

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Abstract

A case of congenital short gut is reported in a 4-month-old boy presenting with failure to thrive. Upper gastrointestinal examination (UGI) with small bowel follow-through (SBFT) demonstrated dilation of the duodenum and jejunum, with rapid transit to rectum. On barium enema (BE), rapid transit of barium was noted to the dilated proximal small bowel seen on UGI/SBFT. Neither study delineated the ileocecal region, and the overall length of bowel appeared short. The diagnosis of congenital short gut was confirmed at surgery. Congenital short-gut syndrome is a rare entity. The diagnosis can be suggested by imaging, but is usually confirmed operatively.

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References

  1. Kern IB, Leece A, Bohane T (1990) Congenital short gut, malrotation, and dysmotility of the small bowel. J Pediatr Gastroenterol Nutr 11:411–415

    CAS  PubMed  Google Scholar 

  2. Erez I, Reish O, Kovalivker M, et al (2001) Congenital short-bowel and malrotation: clinical presentation and outcome of six affected offspring in three related families. Eur J Pediatr Surg 11:331–333

    Article  CAS  PubMed  Google Scholar 

  3. Tiu CM, Chou YH, Chang T (1984) Congenital short bowel. Pediatr Radiol 14:343–345

    CAS  PubMed  Google Scholar 

  4. Wu T-J, Teng R-J, Chang M-H, et al (1992) Congenital short bowel syndrome: report of a case treated with home central parenteral nutrition. J Formos Med Assoc 91:470–472

    CAS  PubMed  Google Scholar 

  5. Park BK (2002) Intestinal transplantation in pediatric patients. Prog Transplant 12:97––113

    PubMed  Google Scholar 

  6. Tanner MS, Smith B, Lloyd JK (1976) Functional intestinal obstruction due to deficiency of argyrophil neurons in the myenteric plexus. Arch Dis Child 51:837–841

    CAS  PubMed  Google Scholar 

  7. Sarimurat N, Celayir S, Elicevik M, et al (1998) Congenital short bowel syndrome associated with appendiceal agenesis and functional intestinal obstruction. J Pediatr Surg 33:666–667

    CAS  PubMed  Google Scholar 

  8. Hamilton JR, Reilly BJ, Morecki R (1969) Short small intestine associated with malrotation. A newly described congenital cause of intestinal malabsorption. Gastroenterology 55:124–135

    Google Scholar 

  9. Aviram R, Erez I, Dolfin TZ, et al (1998) Congenital short-bowel syndrome: prenatal sonographic findings of a fatal anomaly. J Clin Ultrasound 26:106–108

    Article  CAS  PubMed  Google Scholar 

  10. De Backer AI, Parizel PM, De Schepper A, et al (1997) A patient with congenital short small bowel associated with malrotation. J Belge Radiol 80:71–72

    PubMed  Google Scholar 

  11. Iwai N, Yanagihara J, Tsuto T, et al (1985) Congenital short small bowel with malrotation in a neonate. Z Kinderchir 40:371–373

    CAS  PubMed  Google Scholar 

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Authors and Affiliations

  1. Section of Pediatric Radiology, C.S. Mott Children’s Hospital, Room F3503, Department of Radiology, University of Michigan Health System, 1500 East Medical Center Drive, Ann Arbor, MI 48109-0252, USA

    Gauravi Sabharwal & Peter J. Strouse

  2. Division of Pediatric Surgery, C.S. Mott Children’s Hospital, Department of Surgery, University of Michigan Health System, 1500 East Medical Center Drive, Ann Arbor, MI 48109-0052, USA

    Saleem Islam

  3. Division of Pediatric Gastroenterology, C.S. Mott Children’s Hospital, Department of Pediatrics, University of Michigan Health System, 1500 East Medical Center Drive, Ann Arbor, MI 48109-0718, USA

    Najeeb Zoubi

Authors
  1. Gauravi Sabharwal
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  2. Peter J. Strouse
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  3. Saleem Islam
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  4. Najeeb Zoubi
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Corresponding author

Correspondence to Peter J. Strouse.

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Sabharwal, G., Strouse, P.J., Islam, S. et al. Congenital short-gut syndrome. Pediatr Radiol 34, 424–427 (2004). https://doi.org/10.1007/s00247-003-1087-2

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  • DOI: https://doi.org/10.1007/s00247-003-1087-2

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