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Intra-abdominal desmoplastic small round-cell tumour: multiphase CT findings in two children

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Abstract

We report the multiphase CT findings of intra-abdominal desmoplastic small round-cell tumour (DSRCT) in two children. CT showed a huge heterogeneous intraperitoneal mass with or without direct invasion into solid organs such as liver or kidney, extensive intraperitoneal seeding, intratumoural calcification, ascites, and lymphadenopathy. DSRCT should be included in the differential diagnosis of malignant intraperitoneal neoplasm in children. Multiphase CT may be helpful in delineating tumour extent, vascularity and direct invasion into adjacent organs.

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References

  1. Gerald WL, Rosai J (1989) Case 2. Desmoplastic small cell tumor with divergent differentiation. Pediatr Pathol 9:177–183

    CAS  PubMed  Google Scholar 

  2. Lae ME, Roche PC, Jin L, et al (2002) Desmoplastic small round cell tumor: a clinicopathologic, immunohistochemical, and molecular study of 32 tumors. Am J Surg Pathol 26:823–835

    Article  PubMed  Google Scholar 

  3. Sabaté JM, Torrubia S, Roson N, et al (2000) Intra-abdominal desmoplastic small round-cell tumor: a rare cause of peritoneal malignancy in young people. Eur Radiol 10:817–819

    Article  PubMed  Google Scholar 

  4. Outwater E, Schiebler ML, Brooks JJ (1992) Intraabdominal desmoplastic small cell tumor: CT and MR findings. J Comput Assist Tomogr 16:429–432

    CAS  PubMed  Google Scholar 

  5. Pickhardt PJ, Fisher AJ, Balfe DM, et al (1999) Desmoplastic small round cell tumor of the abdomen: radiologic-histopathologic correlation. Radiology 210:633–638

    CAS  PubMed  Google Scholar 

  6. Park DH, Kim KH, Lee EC, et al (1998) Desmoplastic small round cell tumor: radiologic findings. J Korean Radiol Soc 38:843–847

    Google Scholar 

  7. Kim HJ, Ahn HJ, Cho OK (1998) Intraabdominal desmoplastic small round cell tumor: report of two cases. J Korean Radiol Soc 38:875–878

    Google Scholar 

  8. Tateishi U, Hasegawa T, Kusumoto M, et al (2002) Desmoplastic small round cell tumor: imaging findings associated with clinicopathologic features. J Comput Assist Tomogr 26:579–583

    Article  PubMed  Google Scholar 

  9. Kawashima A, Goldman SM, Fishman EK, et al (1994) CT of intraabdominal desmoid tumors: is the tumor different in patients with Gardner's disease? AJR 162:339–342

    Google Scholar 

  10. Busch JM, Kruskal JB, Wu B (2002) Best cases from the AFIP. Malignant peritoneal mesothelioma. Radiographics 22:1511–1515

    PubMed  Google Scholar 

  11. Kim OH, Lee KY (1994) Malignant fibrous histiocytoma of primary omental origin in an infant. Pediatr Radiol 24:285–287

    CAS  PubMed  Google Scholar 

  12. Slasky BS, Bar-Ziv J, Freeman AI, et al (1997) CT appearances of involvement of the peritoneum, mesentery and omentum in Wilms' tumor. Pediatr Radiol 27:14–17

    CAS  PubMed  Google Scholar 

  13. Lynch MA, Cho KC, Jeffrey RB Jr, et al (1988) CT of peritoneal lymphomatosis. AJR 151:713–715

    CAS  Google Scholar 

  14. Choi BI, Lee WJ, Chi JG, et al (1990) CT manifestations of peritoneal leiomyosarcomatosis. AJR 155:799–801

    CAS  Google Scholar 

  15. Chung CJ, Fordham L, Little S, et al (1998) Intraperitoneal rhabdomyosarcoma in children: incidence and imaging characteristics on CT. AJR 170:1385–1387

    CAS  Google Scholar 

  16. Newton HB, Rosenblum MK, Walker RW (1992) Extraneural metastases of infratentorial glioblastoma multiforme to the peritoneal cavity. Cancer 69:2149–2153

    CAS  PubMed  Google Scholar 

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Correspondence to Hyun Woo Goo.

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Kim, J.H., Goo, H.W. & Yoon, C.H. Intra-abdominal desmoplastic small round-cell tumour: multiphase CT findings in two children. Ped Radiol 33, 418–421 (2003). https://doi.org/10.1007/s00247-003-0928-3

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  • DOI: https://doi.org/10.1007/s00247-003-0928-3

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