Abstract
Anomalous origin of one pulmonary artery from the ascending aorta is a rare congenital anomaly. Even more rarely reported is its presence in conjunction with persistent pulmonary hypertension of the newborn (PPHN). We present a case of a full-term infant, initially thought to have PPHN and later found to have anomalous origin of the right pulmonary artery from the ascending aorta. We discuss our management concept which included use of PgE1 infusion to restore fetal circulation prior to surgical treatment in this unique clinical scenario.
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Acknowledgements
We would like to express our gratitude to Dr. William Bates from our Division of Radiology and to our echocardiographic sonographers Celeste Kessler RDCS, Kyle G. West RDCS, Angie Galan RDCS and Megan Ragan RDCS for assisting in the imaging of this patient.
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All procedures performed were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.
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Gupta, A., VanLoozen, D., Polimenakos, A.C. et al. Restoring Fetal Circulation as a Means of Bridging Treatment Prior to Surgical Repair of Anomalous Origin of the Right Pulmonary Artery from the Ascending Aorta with Persistent Pulmonary Hypertension of the Newborn. Pediatr Cardiol 39, 848–851 (2018). https://doi.org/10.1007/s00246-018-1849-0
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DOI: https://doi.org/10.1007/s00246-018-1849-0