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Dextrocardia: Practical Clinical Points and Comments on Terminology

Abstract

Dextrocardia is defined by the authors as a right-sided heart with a base–apex axis directed rightward, resulting from a variation in cardiac development, and not used as a general term indicating any heart in the right chest. Dextrocardia occurs in approximately 0.01% of live births and can be discovered in various clinical settings and at various patient ages. The authors review their experience with dextrocardia, discuss useful clinical points that aid in evaluating complex anatomy, recount the history of dextrocardia terminology, and note the current inconsistent nomenclature.

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Abbreviations

[A,D,D-Nl]:

Situs ambiguous, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries

[A,L,L-Nl]:

Situs ambiguous, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries

[I,D,D-T]:

Situs inversus, atrioventricular discordance, ventriculoarterial discordance, and D-transposition of the great arteries

[I,L,L-Nl]:

Situs inversus, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries

[I,L,L-T]:

Situs inversus, atrioventricular concordance, ventriculoaterial discordance, and L-transposition of the great arteries

[S,D,D-Nl]:

Situs solitus, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries

[S,L,L-T]:

Situs solitus, atrioventricular discordance, ventriculoarterial discordance, and L-transposition of the great arteries

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Correspondence to William N. Evans.

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Evans, W.N., Acherman, R.J., Collazos, J.C. et al. Dextrocardia: Practical Clinical Points and Comments on Terminology. Pediatr Cardiol 31, 1–6 (2010). https://doi.org/10.1007/s00246-009-9516-0

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Keywords

  • Dexiocardia
  • Dextrocardia
  • Heterotaxy
  • Situs inversus
  • Situs solitus