Zusammenfassung
Unter intrinsischen Läsionen der knöchernen Schädelbasis versteht man Erkrankungen, die von den die Schädelbasis bildenden Knochen ausgehen. In erster Linie handelt es sich um Knochentumoren und tumorähnliche Läsionen. Mit wenigen Ausnahmen (Nasennebenhöhlenosteome, Exostosen des äußeren Gehörgangs) sind sie selten. Dieser Beitrag gibt einen Überblick über das CT- und MRT-Erscheinungsbild der aus Sicht der Autoren unter diesem Aspekt noch am häufigsten anzutreffenden raumfordernden Läsionen. Dazu zählen die fibröse Dysplasie, Chordome, Chondrosarkome, die Langerhans-Zell-Histiozytose und das multiple Myelom. Abgrenzt werden müssen Pseudotumoren. Artdiagnostische Zuordnungsmöglichkeiten durch CT und/oder MRT, Differenzialdiagnosen und Diagnosesicherung werden dargelegt.
Abstract
Intrinsic bony lesions of the skull base are diseases which arise within the bones forming the skull base. Mainly they are bone tumours and tumour-like lesions. With the exception of osteomas of the paranasal sinuses and exostoses of the external auditory canal, these lesions occur rarely. This article gives an overview of the appearance of the most common primary bony skull base masses in CT and MRI. From the authors’ point of view these are fibrous dysplasia, chordomas, chondrosarcomas, Langerhans cell histiocytosis and multiple myelomas, which must be differentiated from pseudolesions. The possibilities of CT and MRI in making a specific diagnosis, differential diagnosis and the kind of making the final diagnosis are described.
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Danksagung
Wir bedanken uns bei den Mitarbeitern der Institute für Pathologie der Universitäten Halle bzw. Leipzig für die Zurverfügungstellung der histologischen Diagnosen.
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Kösling, S., Neumann, K. & Brandt, S. CT und MRT bei intrinsischen raumfordernden Läsionen der knöchernen Schädelbasis. Radiologe 49, 598–607 (2009). https://doi.org/10.1007/s00117-008-1802-y
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DOI: https://doi.org/10.1007/s00117-008-1802-y