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Kongenitaler Riesenzellnävus

Indikationen und Techniken der chirurgischen Behandlung

Giant congenital naevus

Indications and techniques for surgical treatment

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Zusammenfassung

Der Begriff „kongenitaler Riesenzellnävus“ bezieht sich nach heutigem Verständnis allgemein auf Hautveränderungen, die sich aus Nävuszellen zusammensetzen, bereits bei der Geburt auffallen und einen Durchmesser von mindestens 20 cm oder mehr im Erwachsenenalter erreichen. Grundsätzlich ist die chirurgische Entfernung solcher Veränderungen deswegen indiziert, weil ein hohes Entartungspotenzial in ihnen steckt. Die chirurgische Herausforderung besteht dabei in der funktionellen und ästhetischen Rekonstruktion nach der Entfernung. Der Beitrag zeigt Inzidenz, Spontanverlauf und Pathologie solcher Riesenzellnävusveränderungen auf. Die Vor- und Nachteile verschiedener Rekonstruktionsverfahren werden dargestellt und ein Algorithmus zum Management dieser potenziell malignen Veränderungen für den Chirurgen aufgestellt.

Abstract

According to current knowledge the term giant congenital naevus is generally applied to skin alterations which consist of naevus cells, that are already conspicuous at birth and reach a diameter of at least 20 cm or more in adulthood. Surgical removal of such alterations is fundamentally indicated because there is high potential for degeneration. The surgical challenge is the functional and aesthetic reconstruction after removal. This article presents the incidence, natural course and pathology of such giant congenital naevus alterations. The advantages and disadvantages of various reconstruction procedures are presented together with an algorithm for management of these potentially malignant alterations.

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Danksagung

Die Autoren danken der Xue-Hong-Dong-Geis- und Hans-Georg-Geis-Stiftung für die Unterstützung.

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Der korrespondierende Autor gibt an, dass kein Interessenkonflikt besteht.

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Authors and Affiliations

  1. Plastisch- und Handchirurgische Klinik, Universitätsklinikum Erlangen, Krankenhausstraße 12, 91054, Erlangen, Deutschland

    J.P. Beier, S. Schnabl, A. Arkudas & R.E. Horch

  2. Pathologisches Institut, Universitätsklinikum Erlangen, Erlangen, Deutschland

    A. Schlabrakowski

  3. Dermatologische Klinik, Universitätsklinikum Erlangen, Erlangen, Deutschland

    J. Bauerschmitz

Authors
  1. J.P. Beier
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  2. S. Schnabl
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  3. A. Arkudas
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  4. A. Schlabrakowski
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  5. J. Bauerschmitz
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  6. R.E. Horch
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Correspondence to J.P. Beier.

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Beier, J., Schnabl, S., Arkudas, A. et al. Kongenitaler Riesenzellnävus. Chirurg 81, 127–133 (2010). https://doi.org/10.1007/s00104-009-1815-8

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  • DOI: https://doi.org/10.1007/s00104-009-1815-8

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