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A surgical case of acute three-channeled aortic dissection in Marfan syndrome

  • Motomi Ando
  • Shinichi Takamoto
  • Yutaka Okita
  • Tetsuo Morota
  • Ritsu Matsukawa
Case Report

Abstract

We surgically treated a 35-year-old male with acute 3- channeled aortic dissection in Marfan syndrome. He had acute type A aortic dissection, and underwent Bentall’s type operation, simultaneous graft replacement of the ascending aorta and total aortic arch. Pain recurred 5 years and 9 months after the first operation. CT scan showed two adjacent false lumens in the descending aorta. The morphology of the first and second dissections was Stanford type A+B. The second dissection was acute. In the second false lumen, a re-entry formation was observed in the abdominal aorta. Because severe pain was persistent, we immediately replaced the descending aorta using a femoro-femoral partial cardiopulmonary bypass. The patient was doing well and was discharged. When pain recurs in a Marfan patient with an aortic dissection, a 3-channeled aortic dissection should be suspected, and we recommend emergency surgery.

Index words

three-channeled aortic dissection first false lumen second false lumen acute dissection Marfan syndrome 

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Copyright information

© The Japanese Society of Thoracic and Cadiovascular Surgery 1998

Authors and Affiliations

  • Motomi Ando
    • 1
  • Shinichi Takamoto
    • 1
  • Yutaka Okita
    • 1
  • Tetsuo Morota
    • 1
  • Ritsu Matsukawa
    • 1
  1. 1.Department of Cardiovascular SurgeryNational Cardiovascular CenterOsakaJapan

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