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Primary monophasic mediastinal, cardiac and pericardial synovial sarcoma: a young man in distress

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Abstract

A 19-year-old male was admitted because of exertional dyspnoea. The imaging studies revealed epicardial, pericardial and mediastinal masses. The tumours could not be resected through a minor thoracotomy, only biopsies could be taken. Analyses led to the final diagnosis of a monophasic synovial sarcoma. The patient preferred a conservative and palliative approach. Three months later he died at home. Autopsy demonstrated dramatic extension of the tumour masses. We conclude this report with a discussion on primary cardiac tumours. (Neth Heart J 2007;15:226-8.)

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References

  • Burke AP, Cowan D, Virmani R. Primary sarcomas of the heart. Cancer 1992;69:387-95.

    Google Scholar 

  • Donsbeck AV, Ranchere D, Coindre JM, Le Gall F, Cordier JF, Loire R. Primary cardiac sarcomas: an immunohistochemical and grading study with long-term follow-up of 24 cases. Histopathology 1999;34:295-304.

    Google Scholar 

  • Nicholson AG, Rigby M, Lincoln C, Meller S, Fisher C. Synovial sarcoma of the heart. Histopathology 1997;30:349-52.

    Google Scholar 

  • Weiss SW, Goldblum JR. Malignant soft tissue tumors of uncertain type. In: Enzinger and Weiss’s soft tissue tumors, 4th ed. St. Louis, MO; Mosby, 2001:1483-509.

  • McGilbray TT, Schulz TK. Clinical picture: Primary cardiac synovial sarcoma. Lancet Oncol 2003;4:283.

    Google Scholar 

  • Turc-Carel C, Dal Cin P, Limon J, Li F, Sandberg AA. Translocation X: 18 in synovial sarcoma. Cancer Genet Cytogenet 1986;23:93-5.

    Google Scholar 

  • Clark J, Rocques P, Crew AJ, Gill S, Shipley J. Chan AM, et al. Identification of novel genes SYT and SSX, involved in the t (X;18) (p11.2; q 11.2) translocation found in synovial sarcoma. Nat Genet 1994;7:502-8.

    Google Scholar 

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Authors and Affiliations

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    C. de Zwaan

Authors
  1. C. de Zwaan
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  2. L. A. F. M. van Garsse
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  3. R. L. H. Jansen
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  4. R. J. van Suylen
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Corresponding author

Correspondence to C. de Zwaan.

Additional information

Department of Cardiology, Maastricht University Hospital, Maastricht, the Netherlands

Department of Cardiothoracic Surgery, Maastricht University Hospital, Maastricht, the Netherlands

Department of Internal Medicine, Maastricht University Hospital, Maastricht, the Netherlands

Department of Pathology, Maastricht University Hospital, Maastricht, the Netherlands

C. de Zwaan Department of Cardiology, Maastricht University Hospital, PO Box 5800, 6202 AZ Maastricht, the Netherlands

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de Zwaan, C., van Garsse, L.A.F.M., Jansen, R.L.H. et al. Primary monophasic mediastinal, cardiac and pericardial synovial sarcoma: a young man in distress. NHJL 15, 226–228 (2007). https://doi.org/10.1007/BF03085986

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