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Plexiform neurofibromatosis presenting as dysphagia

  • Gupta A. K. 
  • Rijuneeta
  • Dey Pranab 
Clinical Report
  • 66 Downloads

Abstract

Plexiform neurofibromatosis is a autosomal dominant disease characterized by multiple cafe aulait spots, cutaneous neurofibromatosis, CMS tumours and skeletal abnormalities. We report a child with plexiform neurofibromatosis presenting with dysphagia, an unsual presentation.

Key words

Plexiform neurofibromatosis dysphagia Head and Neck tumours 

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Copyright information

© Association of Otolaryngologists of India 2006

Authors and Affiliations

  • Gupta A. K. 
    • 1
  • Rijuneeta
    • 1
  • Dey Pranab 
    • 2
  1. 1.Dept. of Otolaryngology and Head and Neck SurgeryPGIMERChandigarh
  2. 2.Department of Cytology Postgraduate Institute of Medical Education and ResearchChandigarh

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