Advertisement

Klinische Neuroradiologie

, Volume 7, Issue 2, pp 93–97 | Cite as

Querschnittssyndrom bei Morbus Ollier

Ein Fallbericht
  • B. Wörner
  • M. Schumacher
Article
  • 33 Downloads

Zusammenfassung

Bei einer Patientin mit bekanntem Morbus Ollier entwickelte sich nach 30jährigem Verlauf ohne neurologische Symptome innerhalb von zwei Jahren ein progredienter sensomotorischer thorakaler Querschnitt bei erheblich eingeengtem Spinalkanal. Bildmorphologische Zeichen einer malignen Entartung bestanden nicht, obwohl der zweite bis siebte Brustwirbelkörper tumorös durchsetzt waren. Ein weiteres großes Enchondrom bestand in der okzipitalen Schädelkalotte, außerdem war der Klivus befallen, was bei Morbus Ollier ungewöhnlicher als beim Mafucci-Syndrom ist.

Transverse myelopathy in Ollier's disease. A case report

Summary

A female patient with Ollier's disease since 30 years developed a paraparesis and a sensoric deficit lower to the fifth thoracal segment during the last 2 years. Imaging revealed no indication of degeneration to malignancy. The vertebral bodies of thoracal spine were affected by tumor masses, inducing symptoms due to compression of the myelon. Another large enchondroma was found in the occipital bone. The clivus was enlarged by a tumor mass, too. Affection of the clivus is uncommon in Ollier's disease, but more frequently described in Mafucci syndrom.

Key Words

Enchondromatosis Ollier's disease Transverse myelopathy 

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

Literatur

  1. 1.
    Adler, C. P., A. Klümper, W. Wenz: Enchondrome aus radiologischer und pathologisch-anatomischer Sicht: Radiologe 19 (1979), 341–349.PubMedGoogle Scholar
  2. 2.
    Brazier, D. J., J. Roberts-Harry, A. Crockard: Intracavemous chondrosarcoma associated with Ollier's disease. Brit. J. Ophthal. 77 (1993), 599–600.PubMedCrossRefGoogle Scholar
  3. 3.
    Chang, S., M. D. Prados: Idenlical twins with Ollier's disease and intracranial gliomas: case report: Neurosurgery 34 (1994), 903–906.PubMedCrossRefGoogle Scholar
  4. 4.
    Collins, P. S., W. Han, L. R. Williams, N. Rich, J. F. Lee, J. L. Villavicencio: Mafueci's syndrome (hemangiomatosis osteolytica): a report of four cases. J. vasc. Surg. 16 (1992), 364–371.PubMedCrossRefGoogle Scholar
  5. 5.
    DeSantos, L. A., H. J. Spjut: Periosteal chondroma: a radiographic spectrum. Skelet. Radiol. 6 (1981), 15.CrossRefGoogle Scholar
  6. 6.
    Ghogawala, Z., M. Moore, R. Strand, W. J. Kupsky, R. M. Scott: Clival chondroma in a child with Ollier's disease. Case report. Pediat. Neurosurg. 17 (1991/1992), 53–56.CrossRefGoogle Scholar
  7. 7.
    Nakayama, Y., Y. Takeno, H. Tsugu, M. Tomonaga: Maffucci's syndrome associated with intracranial chordoma: case report. Neurosurgery 34 (1994), 907–909.PubMedCrossRefGoogle Scholar
  8. 8.
    Neretin, V, V. A. Kiriakov, L. V. Skorochkina, T. V. Loseva: Neurologic manifestations in Ollier's disease. Zh. Nevropat. Psikhiat. 91 (1991), 17–19.Google Scholar
  9. 9.
    Pospiech, J., H. M. Mehdorn, V. Reinhardt, W. Grote: Sellar chondroma in a case of Ollier's disease: Neurochirurgia 32 (1989), 30–35.PubMedGoogle Scholar
  10. 10.
    Rawlings, C. E., D. E. Bullard, P. C. Burger, A. H. Friedmann: A case of Ollier's disease associated with two intracranial gliomas. Neurosurgery 21 (1987), 400–403.PubMedCrossRefGoogle Scholar
  11. 11.
    Schwartz, H. S., N. B. Zimmerman, M. A. Simon, R. R. Wroble, E. A. Millar, M. Bonfiglio. The malignant potential of enchondromatosis. J. Bone Jt Surg. 69-A (1987), 269–274.Google Scholar
  12. 12.
    Traflet, R. F., A. R. Babaria, G. Barolat, H. T. Doan, C. Gonzalez, M. M. Mishkin: Intracranial chondroma in a patient with Ollier's disease. Case report. J. Neurosurg. 70 (1989), 274–276.PubMedCrossRefGoogle Scholar

Copyright information

© Urban & Vogel 1997

Authors and Affiliations

  • B. Wörner
    • 1
  • M. Schumacher
    • 1
  1. 1.Sektion NeuroradiologieUniversitätsklinikFreiburg

Personalised recommendations