A family with Multiple Endocrine Neoplasia Type 1

  • M. R. Lucey
  • S. McCann
  • D. G. Weir


A family of 4 siblings is described in which 3 sisters have Multiple Endocrine Neoplasia Type I (Wermer's Syndrome). All 3 have had Zollinger-Ellison syndrome. One sister in addition had pituitary and parathyroid adenomata, while a second had hyperparathyroidism. It is possible that their father had Zollinger-Ellison syndrome.


Total Gastrectomy Osteogenesis Imperfecta Multiple Endocrine Neoplasia Type Serum Gastrin Islet Cell Tumour 
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Copyright information

© Springer 1983

Authors and Affiliations

  • M. R. Lucey
    • 1
  • S. McCann
    • 1
  • D. G. Weir
    • 1
  1. 1.Department of MedicineSir Patrick Dun's HospitalDublin

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