A family with Multiple Endocrine Neoplasia Type 1
A family of 4 siblings is described in which 3 sisters have Multiple Endocrine Neoplasia Type I (Wermer's Syndrome). All 3 have had Zollinger-Ellison syndrome. One sister in addition had pituitary and parathyroid adenomata, while a second had hyperparathyroidism. It is possible that their father had Zollinger-Ellison syndrome.
KeywordsTotal Gastrectomy Osteogenesis Imperfecta Multiple Endocrine Neoplasia Type Serum Gastrin Islet Cell Tumour
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