A family with Multiple Endocrine Neoplasia Type 1
- 15 Downloads
A family of 4 siblings is described in which 3 sisters have Multiple Endocrine Neoplasia Type I (Wermer's Syndrome). All 3 have had Zollinger-Ellison syndrome. One sister in addition had pituitary and parathyroid adenomata, while a second had hyperparathyroidism. It is possible that their father had Zollinger-Ellison syndrome.
KeywordsTotal Gastrectomy Osteogenesis Imperfecta Multiple Endocrine Neoplasia Type Serum Gastrin Islet Cell Tumour
- Diem, K., Lentner, C. 1970. C. Eds. Scientific Tables. Documenta Geigy. Seventh Ed. Ciba Geigy. p. 748.Google Scholar
- Isanberg, J. I., Walsh, J. H., Grossman, M. T. 1973. Zollinger-Ellison syndrome. Gastroenterology 65, 140–157.Google Scholar
- Schimke, R. N. 1976. Multiple Adenomatosis Syndromes. Advances in Internal Medicine. (Chicago) 21, 249–265.Google Scholar
- Wellbourne, R. B., Polak, J. M., Bloom, S. R., Pearse, A. G. E., Galland, R. R. 1978. Apudomas of the Pancreas. In: Gut Hormones. Ed. S. R. Bloom. Church Livingston. 561–569Google Scholar