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Familial cryptogenic fibrosing alveolitis: a case report

  • J. C. Stinson
  • H. Tomkin
Article

Abstract

A family of seven siblings is described, all of whom, developed finger clubbing during their third decade. Three of the seven developed cryptogenic fibrosing alveolitis (CFA). Of the remaining four siblings, two have died prematurely from conditions possibly associated with cryptogenic fibrosing alveolitis. The youngest two siblings remain asymptomatic at present. This paper reports one of the most concentrated incidences of the rare familial form of CFA.

Keywords

Idiopathic Pulmonary Fibrosis Pulmonary Fibrosis Interstitial Lung Disease Progressive Dyspnoea Fibrosing Alveolitis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer 1992

Authors and Affiliations

  • J. C. Stinson
    • 1
    • 2
  • H. Tomkin
    • 1
  1. 1.Adelaide HospitalDublin 8
  2. 2.Department of Therapeutics, Trinity College Medical School BuildingSt. James’ HospitalDublin 8

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