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The Indian Journal of Pediatrics

, Volume 66, Issue 1, pp 145–147 | Cite as

Stiff man’s syndrome

  • Satyajit Naique
  • Nandkumar Katakdhond
  • S. K. Srivastava
Clinical Brief

Abstract

Myositis ossificans progressiva is an autosomal dominant disease resulting in progressive ossification and skeletal deformities, mainly in the connective tissue of muscle. The diagnosis is based on clinical and radiological findings and demonstration of skeletal malformations. We report a singular case of advanced myositis ossificans progressiva in a fourteen year old male and analyse the natural history, etiopathology, treatment alternatives and prognosis of this crippling disorder.

Key words

Myositis ossificans progressiva Ectople ossification Skeletal malformation Autosomal dominant disorder 

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References

  1. 1.
    Smith, R., RGG, and Woods CG. Myositis ossificans progressiva: Clinical features of eight patients and their response to treatment.Journal of Bone and Jt. Surgery 1976; 58B: 48–57.Google Scholar
  2. 2.
    Lockhart JD, and Burke FG. Myositis ossificans progressiva.Am J Dis Child 1954; 87: 626.Google Scholar

Copyright information

© Dr. K C Chaudhuri Foundation 1999

Authors and Affiliations

  • Satyajit Naique
    • 1
  • Nandkumar Katakdhond
    • 1
  • S. K. Srivastava
    • 1
  1. 1.Department of OrthopedicsK.E.M. HospitalMumbai

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