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Stenosis of the bicuspid aortic valve with systemic lupus erythematosus

  • Masaru Yoshikai
  • Junichi Muraya
  • Hiroya Fujita
Case Report
  • 45 Downloads

Abstract

We herein present a rare case of severe aortic valve stenosis with a bicuspid valve in a patient with systemic lupus erythematosus. The symptoms resulted from aortic valve stenosis, such as chest pain, dyspnea and syncope, which subsided after the insertion of an intra-aortic balloon pump. Thereafter, a calcified bicuspid aortic valve was successfully replaced with a mechanical valve. The pathological findings of the resected valve included irregular fibrotic thickening and marked calcification without any vegetation or thrombus formation. The efficacy of an intra-aortic balloon pump for the relief of symptoms associated with severe aortic valve stenosis indicates its usefulness for such critically ill patients prior to undergoing valvular surgery.

Key words

aortic valve stenosis systemic lupus erythematosus bicuspid aortic valve intra-aortic balloon pump 

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Copyright information

© Japanese Association for Thoracic Surgery 2006

Authors and Affiliations

  • Masaru Yoshikai
    • 1
  • Junichi Muraya
    • 1
  • Hiroya Fujita
    • 1
  1. 1.Department of Cardiovascular SurgeryShin-Koga HospitalKurume, FukuokaJapan

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