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Endocrine Pathology

, Volume 9, Issue 4, pp 375–377 | Cite as

Thirty-year survival with an untreated malignant duodenal somatostatinoma

  • Jan Ulfberg
  • Tibor Tot
  • Erik Wilander
Case Report

Abstract

Gastrointestinal somatostatinomas are rare. Only 56 cases with duodenal origin have been reported in the literature. The long-term course of an untreated tumor like this is unknown.

We report a case of a male patient who lived 30 yr with an untreated metastatic duodenal somatostatinoma. This case suggests that a duodenal somatostatinoma may be of low malignant potential and that expectancy when treating this tumor might be indicated.

Key Words

Somatostatinoma 

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Copyright information

© Humana Press Inc 1998

Authors and Affiliations

  1. 1.Department of PathologyFalun Central HospitalFalunSweden
  2. 2.Department of PathologyUppsala University HospitalUppsalaSweden
  3. 3.Department of Internal MedicineAvesta HospitalAvestaSweden

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