Abstract
Gastrointestinal somatostatinomas are rare. Only 56 cases with duodenal origin have been reported in the literature. The long-term course of an untreated tumor like this is unknown.
We report a case of a male patient who lived 30 yr with an untreated metastatic duodenal somatostatinoma. This case suggests that a duodenal somatostatinoma may be of low malignant potential and that expectancy when treating this tumor might be indicated.
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Ulfberg, J., Tot, T. & Wilander, E. Thirty-year survival with an untreated malignant duodenal somatostatinoma. Endocr Pathol 9, 375–377 (1998). https://doi.org/10.1007/BF02739698
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DOI: https://doi.org/10.1007/BF02739698