The Indian Journal of Pediatrics

, Volume 71, Issue 7, pp 655–657 | Cite as

Mondini dysplasia and pyogenic meningitis

  • Milind S. Tullu
  • Shilpa S. Khanna
  • Jaishree R. Kamat
  • M. V. Kirtane
Clinical Brief


Mondini dysplasia with cerebrospinal fluid leak is a rare cause of recurrent pyogenic meningitis in children. We describe an eleven-year-old female child who presented with the fifth recurrent episode of pyogenic meningitis and unilateral sensorineural deafness. Mondini dysplasia of the inner ear with CSF-perilymph fistula was proven on an HRCT of the temporal bone and MRI. Successful operative intervention was undertaken to close the defect. Though rare, Mondini dysplasia should be considered as a cause of recurrent meningitis in children, especially if they have sensorineural deafness

Key words

Cerebrospinal fluid Cochlea Deafness Inner ear Temporal bone 


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Copyright information

© Department of Pediatrics All India Institute Of Medical Science 2004

Authors and Affiliations

  • Milind S. Tullu
    • 2
  • Shilpa S. Khanna
    • 2
  • Jaishree R. Kamat
    • 2
  • M. V. Kirtane
    • 1
    • 2
  1. 1.Department of OtorhinolaryngologySeth G. S. Medical College and KEM Hospital, ParelMumbai, MaharashtraIndia
  2. 2.Department of PediatricsSeth G. S. Medical College and KEM Hospital, ParelMumbai, MaharashtraIndia

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