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The Indian Journal of Pediatrics

, Volume 70, Issue 10, pp 837–838 | Cite as

Aniridia and wilm’s tumor

  • Manisha Nada
  • K. N. Rattan
  • Sarita Magu
  • Sanjeev Parshad
Clinical Brief

Abstract

Aniridia (absence of iris) is a congenital, bilateral, uncommon panocular disorder. Whereas the occurrence of aniridia in the general population is 1:50000, it is present in about 1 in 70 patients with Wilm’s tumor. This aniridia is sporadic and Wilm’s tumor in these cases presents at an unusually early age. Aniridia was present in two cases out of 60 cases of Wilm’s tumor operated at PGIMS, Rohtak. Both cases presented below two years of age. The recognition of a child with sporadic aniridia should alert to the increased risk of development of Wilm’s tumor.

Key words

Aniridia Wilm’s tumor WAGR syndrome 

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Copyright information

© Dr. K C Chaudhuri Foundation 2003

Authors and Affiliations

  • Manisha Nada
    • 1
  • K. N. Rattan
    • 2
  • Sarita Magu
    • 3
  • Sanjeev Parshad
    • 4
  1. 1.Department of OphthalmologyPt. B.D. Sharma PGIMSRohtak, HaryanaIndia
  2. 2.Department of Pediatric SurgeryPt. B.D. Sharma PGIMSRohtak, HaryanaIndia
  3. 3.Department of RadiologyPt. B.D. Sharma PGIMSRohtak, HaryanaIndia
  4. 4.Department of SurgeryPt. B.D. Sharma PGIMSRohtak, HaryanaIndia

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