Pediatric Radiology

, Volume 4, Issue 4, pp 257–260 | Cite as

Congenital eventration of the septum transversum

A rare form of congenital diaphragmatic anomaly
  • C. A. Poole
  • M. I. Rowe
  • R. M. Fojaco
  • H. A. Wexler
Case Reports


A rare congenital anomaly of the central anterior diaphragm is presented. The anomaly consisted of a severe eventration of the septum transversum, and was associated with a cleft lower sternum and congenital heart disease. The pericardium and diaphragm were intact. This anomaly, which can be timed to the seventh week of gestation, is felt to represent a variant of the “pentad syndrome”. It is probably the second such form of this syndrome to appear in the literature.

Key words

Diaphragm congenital anomaly eventration Pentad syndrome 


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Copyright information

© Springer-Verlag 1976

Authors and Affiliations

  • C. A. Poole
    • 1
  • M. I. Rowe
    • 1
  • R. M. Fojaco
    • 1
  • H. A. Wexler
    • 1
  1. 1.Department of RadiologyUniversity of Miami School of MedicineMiamiU.S.A.

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