Skip to main content
Log in

Gaucher disease of the liver: CT appearance

  • Short Reports
  • Published:
Pediatric Radiology Aims and scope Submit manuscript

Abstract

We present a child with Gaucher disease with hepatic involvement that caused portal hypertension. Computerized tomography (CT) showed distortion of liver parenchyma and central necrosis of the liver.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

References

  1. Brady RO, Barranger JA (1982) Glucosyl ceramide lipidosis: Gaucher's disease. In: Stanbury JB, Wyngaarden JB, Fredrickson DS, Goldstein JL, Brown MS (eds) The metabolic basis of inherited disease, 5th ed. McGraw-Hill, New York, p 842

    Google Scholar 

  2. Fellows KE, Grand RJ, Colodny AH, Orsini EN, Crocker AC (1975) Combined portal and vena caval hypertension in Gaucher disease: the value of preoperative venography. J Pediatr 87: 739

    Article  CAS  PubMed  Google Scholar 

  3. Sales JEL, Hunt AH (1970) Gaucher's disease and portal hypertension. Br J Surg 57: 225

    CAS  PubMed  Google Scholar 

  4. Shaldon S, Sherlock S (1962) Portal hypertension in the myeloproliferative syndrome and the reticuloses. Am J Med 32: 758

    Article  CAS  PubMed  Google Scholar 

  5. Aderka, D, Garfinkel D, Rothem A, Pinkhas J (1982) Fatal bleeding from esophageal varices in a patient with Gaucher's disease. Am J Gastroenterol 77: 838

    CAS  PubMed  Google Scholar 

  6. Morrison AN, Lane M (1955) Gaucher's disease with ascites: a case report with autopsy findings. Ann Intern Med 42: 1321

    CAS  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Rights and permissions

Reprints and permissions

About this article

Cite this article

Glass, R.B.J., Poznanski, A.K., Young, S. et al. Gaucher disease of the liver: CT appearance. Pediatr Radiol 17, 417–418 (1987). https://doi.org/10.1007/BF02396621

Download citation

  • Received:

  • Accepted:

  • Issue Date:

  • DOI: https://doi.org/10.1007/BF02396621

Keywords

Navigation