Pediatric Radiology

, Volume 15, Issue 2, pp 141–143 | Cite as

A case of lethal congenital dwarfism with accelerated skeletal maturation

  • S. Blomstrand
  • I. Claësson
  • J. Säve-Söderbergh
Short Reports


Details of a female infant, who was born after 29 weeks gestation and who died within minutes of birth, are presented. The infant was hydropic, showed macroglossia and had very short limbs with normal sized hands and feet. Apart from a preductal aortic coarctation the pathological findings were confined to the skeleton. The radiographical and histological findings are described in detail; they differ from those of previous studies of similar conditions.


Public Health Similar Condition Pathological Finding Histological Finding Aortic Coarctation 
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Copyright information

© Springer-Verlag 1985

Authors and Affiliations

  • S. Blomstrand
    • 1
  • I. Claësson
    • 3
  • J. Säve-Söderbergh
    • 2
  1. 1.Department of PediatricsChildrens Hospital, Östra SjukhusetSweden
  2. 2.Department of Pathology Östra SjukhusetUniversity of GöteborgGöteborgSweden
  3. 3.Department of RadiologyChildren's Hospital Östra SjukhusetGöteborgSweden

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