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Dyskinetic cilia syndrome: clinical, radiographic and scintigraphic findings

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Abstract

The clinical, electron microscopic and radiographic data of 9 patients with dyskinetic cilia syndrome (DCS) are presented. Scintigraphic evaluation of mucociliary dynamics in six patients showed evidence of dyskinesia. Ventilation and perfusion studies were performed to evaluate obstructive lung disease. Retrospectively, bronchiectasis could be detected in 77% of the patients by analysis of the chest radiograph and lung scintigraphy, and bronchography potentially avoided in the seven patients who underwent this procedure.

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Authors and Affiliations

  1. Department of Pediatrics, Pulmonary Division, University of Utah, School of Medicine, Salt Lake City, USA

    S. Reyes de la Rocha

  2. Departments of Pathology and Pediatrics, Primary Children's Medical Center, University of Utah, School of Medicine, Salt Lake City, USA

    T. J. Pysher

  3. Department of Radiology, Oklahoma Children's Memorial Hospital, University of Oklahoma Health Sciences Center, Oklahoma City, Oklahoma

    J. C. Leonard

  4. Section of Pulmonary Diseases, Oklahoma Childrens Memorial Hospital, P.O. Box 26307, 73126, Oklahoma City, OK, USA

    S. Reyes de la Rocha

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  1. S. Reyes de la Rocha
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  2. T. J. Pysher
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  3. J. C. Leonard
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Reyes de la Rocha, S., Pysher, T.J. & Leonard, J.C. Dyskinetic cilia syndrome: clinical, radiographic and scintigraphic findings. Pediatr Radiol 17, 97–103 (1987). https://doi.org/10.1007/BF02388082

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  • DOI: https://doi.org/10.1007/BF02388082

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