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Pediatric Radiology

, Volume 16, Issue 4, pp 302–305 | Cite as

Congenital hepatic fibrosis with saccular dilatation of intrahepatic bile ducts and infantile polycystic kidneys

  • C. H. Davies
  • D. A. Stringer
  • H. Whyte
  • A. Daneman
  • K. Mancer
Originals

Abstract

A case report is presented of a child who died in the neonatal period and who had the sonographic findings of multiple, tubular, fluid-filled spaces in the liver characteristic of Caroli's disease. There was an echodense renal cortex and pyramids. Necropsy findings were consistent with Caroli's disease but the liver also showed evidence of congenital hepatic fibrosis and there was infantile type polycystic disease of the kidneys.

Keywords

Public Health Bile Duct Pyramid Neonatal Period Hepatic Fibrosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag 1986

Authors and Affiliations

  • C. H. Davies
    • 1
  • D. A. Stringer
    • 1
  • H. Whyte
    • 2
  • A. Daneman
    • 1
  • K. Mancer
    • 3
  1. 1.Department of RadiologyThe Hospital for Sick Children and University of TorontoTorontoCanada
  2. 2.Department of Paediatrics (Division of Neonatology)The Hospital for Sick Children and University of TorontoTorontoCanada
  3. 3.Department of PathologyThe Hospital for Sick Children and University of TorontoTorontoCanada

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