Abstract
Perforation of the duodenum is an uncommon, but serious complication which may occur in children with dermatomyositis. In this disease vasculitis may involve the bowel to a variable extent and result in radiologic manifestations of intestinal injury ranging from benign pneumatosis intestinalis to signs of bowel perforation. We report two children with dermatomyositis in whom perforation of the second portion of the duodenum occurred. This serious complication should be considered in any child with dermatomyositis when extraluminal gas is suspected on abdominal radiographs.
Similar content being viewed by others
References
Bohan A, Peter JB (1975) Polymyositis and dermatomyositis. N Engl J Med 344: 407
Carpenter S, Karpati G, Rotham S, Watters G (1976) The childhood type of dermatomyositis. Neurology CNY 26: 952
Pachman LM, Cooke N (1980) Juvenile dermatomyositis: A clinical and immunologic study. J Pediatr 96: 226
Banker BQ, Victor M (1966) Dermatomyositis (systemic angiopathy) of childhood. Medicine (Baltimore) 45: 261
Kleckner FS (1970) Dermatomyositis and its manifestations in the gastrointestinal tract. Am J Gastroenterol 53: 141
Oliveros MA, Herbst JJ, Lester PD, Ziter FA (1973) Pneumatosis intestinalis in childhood dermatomyositis. Pediatrics 52: 711
Hanson V (1976) Dermatomyositis, Scleroderma and polyarteritis nodosa. Clin Rheum Dis 2: 445
Fischer TJ, Cipel L, Stiehm ER (1978) Penumatosis intestinalis associated with fatal childhood dermatomyositis. Pediatrics 6: 127
Mueller CR, Morehead R, Alter AJ, Michener W (1972) Pneumatosis intestinalis in collagen disorders. AJR 115: 300
Braunstein EM, White SJ (1980) Pneumatosis intestinalis in dermatomyositis. Br J Radiol 53: 1011
Meyers MA (1974) Radiological features of the spread and localization of extraperitoneal gas and their relationship to its source. Radiology 111: 17
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Magill, H.L., Hixson, S.D., Whitington, G. et al. Duodenal perforation in childhood dermatomyositis. Pediatr Radiol 14, 28–30 (1984). https://doi.org/10.1007/BF02386727
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF02386727