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Radiological findings in three cases of persistent Müllerian duct syndrome

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Abstract

We report three cases of persistent Müllerian duct syndrome, which is a rare form of inherited male pseudohermaphroditism characterized by the presence of a uterus and tubes in otherwise normally virilized 46,XY males. We emphasize the usefulness of ultrasonographic study of the pelvis and inguinal areas in the preoperative diagnosis, which is difficult. We recommend that ultrasound be performed routinely in bilaterally cryptorchid patients.

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Authors and Affiliations

  1. Radiology Department, Saint Vincent de Paul Hospital, 82 avenue Denfert-Rochereau, F-75014, Paris, France

    C. Adamsbaum, Y. Rolland & G. Kalifa

  2. Ecole Normale Supérieure, Unité de Recherches sur l'Endocrinologie du Développement (INSERM), Montrouge, France

    N. Josso

Authors
  1. C. Adamsbaum
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  2. Y. Rolland
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  3. N. Josso
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  4. G. Kalifa
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Adamsbaum, C., Rolland, Y., Josso, N. et al. Radiological findings in three cases of persistent Müllerian duct syndrome. Pediatr Radiol 23, 55–56 (1993). https://doi.org/10.1007/BF02020225

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  • DOI: https://doi.org/10.1007/BF02020225

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