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Beckwith-Wiedemann syndrome: Development of nephroblastoma during the surveillance period

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Abstract

Two children, with Beckwith-Wiedemann syndrome and hemihypertrophy who were followed by ultrasonography, developed a large nephroblastoma in the interval between two abdominal ultrasound examinations. The customarily suggested bi-annual examinations are not frequent enough and may give physicians and parents a false sense of security.

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Author notes

  1. E. M. Azouz MD

    Present address: Department of Radiology, McGill University, 2300 Tupper Street, H3H 1P3, Montreal, Quebec, Canada

Authors and Affiliations

  1. Montreal Children's Hospital, Montreal, Quebec, Canada

    E. M. Azouz MD

  2. Miller Children's Hospital, Long Beach, California, USA

    E. J. Larson, J. Patel & M. T. Gyepes

Authors
  1. E. M. Azouz MD
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  2. E. J. Larson
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  3. J. Patel
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  4. M. T. Gyepes
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Additional information

Presented in part, Society for Pediatric Radiology 32nd annual meeting, San Antonio, Texas, April 7, 1989

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Azouz, E.M., Larson, E.J., Patel, J. et al. Beckwith-Wiedemann syndrome: Development of nephroblastoma during the surveillance period. Pediatr Radiol 20, 550–552 (1990). https://doi.org/10.1007/BF02011388

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  • DOI: https://doi.org/10.1007/BF02011388

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