Abstract
Leigh's disease, also known as subacute necrotizing encephalomyelopathy, is a rare progressive neurological disorder of childhood that was first described by Leigh in 1951. Diagnosis of this disease can be difficult because onset is usually insidious and can present with a number of different focal findings, however diagnostic imaging has been shown to be of benefit in this regard [1–5]. We present a patient with Leigh's disease in whom serial MR imaging studies helped to make the diagnosis and also demonstrated the dynamic characteristic of this disease process.
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References
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Manzi, S.V., Hager, K.H., Murtagh, F.R. et al. MR imaging in a patient with Leigh's disease (subacute necrotizing encephalomyelopathy). Pediatr Radiol 21, 62–63 (1990). https://doi.org/10.1007/BF02010818
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DOI: https://doi.org/10.1007/BF02010818