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Primary alveolar capillary dysplasia

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Abstract

We describe two neonates with a lethal form of pulmonary maldevelopment. Both infants had bilateral dysplastic immature lungs with poor capillary formation and lack of alveolar development. This rare entity should be considered in the differential diagnosis of a newborn infant with mild diffuse radiographic pulmonary abnormality and severe respiratory distress.

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Authors and Affiliations

  1. University of Pittsburgh School of Medicine, Pittsburgh, PA, USA

    B. Newman

  2. Department of Radiology, Children's Hospital of Pittsburgh, One Children's Place, 15213, Pittsburgh, PA, USA

    B. Newman

  3. Department of Pathology, Children's Hospital of Pittsburgh, Pittsburgh, PA, USA

    E. Yunis

Authors
  1. B. Newman
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  2. E. Yunis
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Newman, B., Yunis, E. Primary alveolar capillary dysplasia. Pediatr Radiol 21, 20–22 (1990). https://doi.org/10.1007/BF02010807

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  • DOI: https://doi.org/10.1007/BF02010807

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