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Pediatric Radiology

, Volume 13, Issue 6, pp 313–318 | Cite as

Biliary disease in metachromatic leukodystrophy

  • Linda Heier
  • A. Daneman
  • J. Alexander Lowden
  • E. Cutz
  • Susan Craw
  • D. J. Martin
Originals

Abstract

This paper illustrates the previously unreported sonographic changes in the biliary tract in metachromatic leukodystrophy (MLD). Gallbladder wall thickening due to sulfatide deposition, intraluminal globules of sulfatide or papillomatosis may cause symptoms referrable to the biliary tract in these patients. A series of patients whom, we have studied is briefly alluded to in order to bring to the attention of the radiologist MLD as a rare cause of biliary disease in children.

Key words

Biliary tract Metachromatic leukodystrophy Ultrasound 

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Copyright information

© Springer-Verlag 1983

Authors and Affiliations

  • Linda Heier
    • 1
  • A. Daneman
    • 1
  • J. Alexander Lowden
    • 2
  • E. Cutz
    • 3
    • 4
  • Susan Craw
    • 1
  • D. J. Martin
    • 1
  1. 1.Department of Radiologythe Hospital for Sick ChildrenTorontoCanada
  2. 2.Department of Pediatricsthe Hospital for Sick ChildrenTorontoCanada
  3. 3.Department of Pathologythe Hospital for Sick ChildrenTorontoCanada
  4. 4.University of TorontoTorontoCanada

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