Abstract
Five boys who had Noonan's syndrome and lymphatic abnormalities are reported. The youngest boy had clinical lymphoedema and the other four showed dermal backflow after interdigital injection of Patent Blue indicating impairment of flow along the superficial lymphatics. One boy had severe bilateral chylothorax. The lymphographic findings in four of these boys are reported.
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Lanning, P., Similä, S., Suramo, I. et al. Lymphatic abnormalities in Noonan's syndrome. Pediatr Radiol 7, 106–109 (1978). https://doi.org/10.1007/BF00975679
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DOI: https://doi.org/10.1007/BF00975679