Abstract
Rupture of the thoracic aorta in a 12-year-old boy with Ehlers-Danlos syndrome and his sudden death are discussed. A review of the literature substantiates the rarity of major vascular catastrophies of any sort in children.
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References
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Blickman, J.G., Griscom, N.T. Aortic rupture in a previously undiagnosed case of the Ehlers-Danlos syndrome. Pediatr Radiol 12, 86–88 (1982). https://doi.org/10.1007/BF00972439
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DOI: https://doi.org/10.1007/BF00972439