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Primitive Neuroectodermal Tumor (PNET) of the Endometrium

  • Raiana Santos Lins
  • Elvys dos Santos PereiraEmail author
  • Thamyres de Almeida Romeiro
  • Alline de Carli Bastos dos Santos
  • Jocela Cristina dos Santos
Case Report
  • 19 Downloads

Abstract

Primitive neuroectodermal tumor (PNET) is a rare and highly aggressive neoplasm that originates in neural crest neuroectodermal cells. It presents a bimodal distribution, which can affect both young and postmenopausal women. About 30% of patients present metastatic disease at the moment of diagnosis, and their survival in 2 years ranges from 25 to 60%. In this report, we describe the case of a 42-year-old patient with a history of vaginal bleeding and a growing tumor compromising the endometrium, initially diagnosed as an endometrial adenocarcinoma, which immunohistochemistry posteriorly revealed a PNET of the endometrium. She was treated with neoadjuvant chemotherapy but had an unfortunate evolution and died.

Notes

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Informed consent

Informed consent was obtained from the patient whose case was reported in this manuscript.

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Copyright information

© Association of Gynecologic Oncologists of India 2019

Authors and Affiliations

  • Raiana Santos Lins
    • 1
  • Elvys dos Santos Pereira
    • 1
    Email author
  • Thamyres de Almeida Romeiro
    • 1
  • Alline de Carli Bastos dos Santos
    • 2
  • Jocela Cristina dos Santos
    • 3
  1. 1.School of MedicineFederal University of AlagoasMaceióBrazil
  2. 2.Department of OncologyUniversity Hospital Professor Alberto AntunesMaceióBrazil
  3. 3.Department of Surgical OncologyUniversity Hospital Professor Alberto AntunesMaceióBrazil

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