This is a case report of a 28-year female with aggressive angiomyxoma who presented with recurrent vulval swelling for which she was operated four times. First time, at the age of 19 years thinking it to be a Bartholin’s duct cyst, that on histopathology found to be angiomyxoma. Swelling recurred as left labial mass within a year of surgery. Second time, she underwent wide excision of the left labial mass, and on immunohistochemistry, it was positive for estrogen and progesterone receptors for which she was offered hormonal treatment, but she denied. Third time, she underwent robotic surgery because upper extent of tumor was deep in the pelvis and was not approachable by perineal route. After 2 years, swelling recurred again for which she got operated fourth time after her pregnancy. Now she has been given GnRH agonist and is being followed up for recurrence.
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Conflict of interest
The authors declare no conflict of interest whatsoever arising out of the publication of this manuscript.
Patient has given her informed consent for the case report to be published.
This study does not contain any studies with human participants or animals performed by any of the authors.
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