Diagnostic dental radiographs not allowed! A child with ataxia telangiectasia
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Ataxia telangiectasia (AT) is a rare neurodegenerative condition which has not previously been reported in the dental literature. It is a life threatening and debilitating disorder of progressive cerebellar ataxia and choreoathetosis, progressive oculocutaneous telangiectasias, immunodeficiency with susceptibility to sinopulmonary infections, impaired organ maturation, X-ray hypersensitivity, and a high incidence of malignancies. Of importance in dentistry is the contra-indication for taking diagnostic radiographs.
A 5-year-old girl with AT was referred by her paediatrician for dental care as she had never been seen by a dentist. She presented with caries affecting a number of primary teeth. Diagnostic radiographs could not be taken due to her X-ray hypersensitivity.
She was given antibiotic prophylaxis for dental treatment under general anaesthetic. She had composite restorations, stainless steel crowns and extractions completed.
She has been reviewed for over 2 years with ongoing enhanced prevention.
This case reports a rare condition in which diagnostic dental radiographs are contra-indicated.
KeywordsAtaxia telangiectasia Radiographs
I would like to extend a large thank you to the family of this girl who have supported the publication of their daughters’ medical and dental findings.
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