Limbic encephalitis-like presentation in neuromyelitis optica spectrum disorder: a case report
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Limbic encephalitis is a syndrome characterized by memory loss, psychiatric symptoms and convulsion, and typical brain lesions are located in mesial temporal lobe. Once known almost always associated with cancer, limbic encephalitis is now considered as a clinical syndrome of autoimmune encephalitis despite whether cancer related or not .
Neuromyelitis optica (NMO) is a rare idiopathic inflammatory disorder of the central nervous system (CNS) with the predominant involvement of the optic nerves and spinal cord having disease-specific autoantibody against aquaporin-4 protein (AQP4-Ab). Various brain syndromes with distinctive brain lesions in patients with NMO have been reported that area of postrema syndrome, acute brainstem syndrome, acute narcolepsy/diencephalic syndrome and symptomatic cerebral syndrome were studied with brain MRI findings . However, limbic encephalitis syndrome and the medial temporal lobe lesions have never been reported in NMOSD. We herein...
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The authors declare that they have no conflict of interest.
This article does not contain any studies with human participants or animals performed by any of the authors.
The informed consent was obtained from the patient.
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