CEN Case Reports

, Volume 6, Issue 2, pp 132–135 | Cite as

Primary Ewing sarcoma of the kidney: a case report and treatment review

  • Muhammad Sadiq
  • Iftikhar AhmadEmail author
  • Jamila Shuja
  • Khushnaseeb Ahmad
Case report


Ewing sarcomas/primitive neuroectodermal tumors (ES/PNET) of the kidney are rarely found high-grade malignant tumors, offering poor prognosis. Although established treatment guidelines for ES of kidney are scarce, a multi-modality treatment approached is typically implemented. Herein, we report a 14-year-old female patient with ES of right kidney. Post-nephrectomy disease recurrence was treated with chemotherapy (i.e., vincristine, doxorubicin and cyclophosphamide); marked reduction in tumor size (i.e., from 18.5 × 11.3 cm2 to 3.7 × 2.2 cm2; ~96% reduction in size) as per computed tomography images was observed. We present our treatment experience and review from the available literature.


Chemotherapy Disease recurrence Ewing sarcoma kidney Radiotherapy Nephrectomy 


Compliance with ethical standards

Conflict of interest

It is declared that the results presented in this paper have not been published previously in whole or part. Furthermore, the authors have no conflict of interest.


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Copyright information

© Japanese Society of Nephrology 2017

Authors and Affiliations

  1. 1.Center for Nuclear Medicine and Radiotherapy (CENAR)QuettaPakistan

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