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Granulosa Cell Tumor of the Ovary Accompanying with Ollier’s Disease: First Case of Contralateral Presentations

  • Amirmohsen Jalaeefar
  • Mohammad Shirkhoda
  • Amirsina SharifiEmail author
  • Mohsen Sfandbod
Case Report
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Abstract

Objective

Granulosa cell tumor (GCT) is a rare entity of ovarian malignancies. Juvenile GCT is considered a malignant tumor with an indolent course and tendency toward late recurrence. However, the association of this tumor and multiple enchondromas has been reported.

Case Presentation

A 17-year-old female with abnormal uterine bleeding was referred to our center. Ultrasonographic evaluation revealed a mass with origin in right ovary. Patient was worked up to undergo salpingo-oophorectomy, she felt a dull pain in her left lower limb. X-ray imaging was indicative for Ollier’s disease at the distal part of femur and proximal part of tibia. Postoperative pathological review was compatible with juvenile granulosa tumor of the right ovary.

Conclusion

This case was the first of its kind that ovarian tumor was contralateral to the side involved by enchondromatosis.

Keywords

Granulosa cell tumor Ollier’s disease Maffucci syndrome Multiple enchondromatosis 

Notes

Compliance with Ethical Standards

Conflict of interest

All authors declare that there is no conflict of interest to disclose.

Human Participants and/or Animals

All parts of Declaration of Helsinki have been applied.

Informed Consent

The patient gave us written consent of her inclusion in the study.

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Copyright information

© Federation of Obstetric & Gynecological Societies of India 2019

Authors and Affiliations

  • Amirmohsen Jalaeefar
    • 1
  • Mohammad Shirkhoda
    • 1
  • Amirsina Sharifi
    • 2
    Email author
  • Mohsen Sfandbod
    • 3
  1. 1.Department of Surgical Oncology, Cancer InstituteTehran University of Medical SciencesTehranIran
  2. 2.Sina Trauma and Surgery Research Center, Sina HospitalTehran University of Medical SciencesTehranIran
  3. 3.Tehran University of Medical SciencesTehranIran

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