Granulosa Cell Tumor of the Ovary Accompanying with Ollier’s Disease: First Case of Contralateral Presentations
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Granulosa cell tumor (GCT) is a rare entity of ovarian malignancies. Juvenile GCT is considered a malignant tumor with an indolent course and tendency toward late recurrence. However, the association of this tumor and multiple enchondromas has been reported.
A 17-year-old female with abnormal uterine bleeding was referred to our center. Ultrasonographic evaluation revealed a mass with origin in right ovary. Patient was worked up to undergo salpingo-oophorectomy, she felt a dull pain in her left lower limb. X-ray imaging was indicative for Ollier’s disease at the distal part of femur and proximal part of tibia. Postoperative pathological review was compatible with juvenile granulosa tumor of the right ovary.
This case was the first of its kind that ovarian tumor was contralateral to the side involved by enchondromatosis.
KeywordsGranulosa cell tumor Ollier’s disease Maffucci syndrome Multiple enchondromatosis
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Conflict of interest
All authors declare that there is no conflict of interest to disclose.
Human Participants and/or Animals
All parts of Declaration of Helsinki have been applied.
The patient gave us written consent of her inclusion in the study.
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