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Journal of Maxillofacial and Oral Surgery

, Volume 18, Issue 2, pp 210–216 | Cite as

Parry Romberg Syndrome: Literature Review and Report of Three Cases

  • N. Girish KumarEmail author
  • Brig S. Maurya
  • Col S. Sudeep
Clinical Paper
  • 30 Downloads

Abstract

Parry Romberg Syndrome or Progressive Hemifacial Atrophy is a rare disease usually affecting one side of face with loss of soft and hard tissues. The disease appears suddenly and is usually self-limiting in 2–10 years time. The loss of soft and hard tissue leads to aesthetic and functional deficits which are compounded by the presence of associated symptoms like neuralgia, migraine, epilepsy and ocular involvement. The degree of deformity depends on the age at which the disease manifests first; the younger the age, the more severe the deformity. These patients undergo severe psychological trauma and social problems. The exact etiology is not known, and treatment is largely cosmetic. A report of three cases and a literature review is presented.

Keywords

Parry Romberg Syndrome Progressive Hemifacial Atrophy Dermal fat graft Porous polyethylene implant Temporalis myofascial flap 

Notes

Acknowledgements

Funding was provided by Government.

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Copyright information

© The Association of Oral and Maxillofacial Surgeons of India 2018

Authors and Affiliations

  1. 1.Department of Oral and Maxillofacial SurgeryPMS College of Dental Science and ResearchThiruvananthapuramIndia
  2. 2.Command HospitalChandimandirIndia
  3. 3.Command Military Dental CentreChandimandirIndia

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