Journal of Echocardiography

, Volume 14, Issue 1, pp 42–44 | Cite as

Unusual combination: Ebstein’s anomaly and hypertrophic obstructive cardiomyopathy

  • Wei-Chieh LeeEmail author
  • Morgan Fu
  • Hsiu-Yu Fang
Case image in cardiovascular ultrasound

Case report

A 48-year-old female gradually experienced dyspnea on exertion for 2 months. She was otherwise healthy and did not have any medical history. She felt shortness of breath when performing heavy work and heavy sweating, but she denied orthopnea, paroxysmal nocturnal dyspnea, edema, and fever. Auscultation could detect grade III mid-systolic murmur over the left lower sternal border to the apex. With deep inspiration, systolic murmur became louder at the left lower sternal border. When standing, systolic murmur became louder at the apex. Electrocardiography showed a right bundle branch block and right atrial enlargement. Chest radiography showed cardiomegaly and pulmonary congestion. Transthoracic echocardiography showed thick interventricular sputum and left ventricular posterior wall (Fig.  1a; Supplemental Video S1). Parasternal long-axis view also noted eccentric mitral regurgitation to inferior wall due to the influence of systolic anterior motion of anterior mitral...


Hypertrophic Cardiomyopathy Tricuspid Valve Left Ventricular Outflow Tract Tricuspid Annular Plane Systolic Excursion Right Bundle Branch Block 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


Compliance with ethical standards

Conflict of interest

Dr. Wei-Chieh Lee, Dr. Morgan Fu, and Dr. Hsiu-Yu Fang declare that they have no conflicts of interest.

Ethical approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards.



Supplementary material

12574_2016_273_MOESM1_ESM.avi (1 mb)
Supplemental Video S1: Transthoracic echocardiography: thick interventricular sputum and left ventricular posterior wall (AVI 1074 kb)

Supplemental Video S2: Hypertrophic obstructive cardiomyopathy with turbulent flow was noted at the subaortic region (AVI 1539 kb)


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Copyright information

© Japanese Society of Echocardiography 2016

Authors and Affiliations

  1. 1.Division of Cardiology, Department of Internal Medicine, Kaohsiung Chang Gung Memorial HospitalChang Gung University College of MedicineKaohsiung CityTaiwan, ROC

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