Journal of Echocardiography

, Volume 12, Issue 4, pp 138–141 | Cite as

Role of cardiovascular echo in patients with Takayasu arteritis

  • Kazuhiro NishigamiEmail author
Review Article



Takayasu arteritis is an important differential diagnosis in young female patients presenting with fever, fatigue, hypertension, and/or neck pain.

Echocardiographic features

Aortic arch branch vessels are frequently affected and the carotid artery can have diffuse, homogeneous wall thickening, known as the ‘macaroni sign’. The descending aorta can be stenotic with ‘pseudo-coarctation’.


Cardiovascular echo plays an important role in the screening and characterization of arterial lesions in patients with Takayasu arteritis.


Cardiovascular echo Takayasu arteritis Aorta Carotid artery 


Conflict of interest

Kazuhiro Nishigami has received honoraria of $1000 or less as a lecture fee from the following companies: Astellas Pharma Inc., AstraZeneca K.K., Bayer Yakuhin Ltd., Boehringer Ingelheim Japan Inc., Kowa Pharmaceutical Co., Ltd., MSD K.K., Shionogi & Co., Ltd., Novartis Pharma K.K., Tanabemitsubishi Pharmaceutical Co., Ltd. and Takeda Pharmaceutical Co., Ltd.

Supplementary material

Supplementary material 1 (AVI 1140 kb). Movie A. Long-axis 2-dimensional image of the descending aorta showing diffuse stenosis of the aorta dorsal to the heart

12574_2014_232_MOESM2_ESM.avi (1.1 mb)
Supplementary material 2 (AVI 1140 kb). Movie B. Long-axis 2-dimensional image of the main pulmonary artery showing its dilatation

Supplementary material 1 (AVI 4001 kb). Movie C. Longitudinal image of the common carotid artery showing that the thickened wall shuffles forward

Supplementary material 1 (AVI 774 kb). Movie D. Color Doppler image in the long-axis of the left ventricle showing aortic regurgitation


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Copyright information

© Japanese Society of Echocardiography 2014

Authors and Affiliations

  1. 1.Department of Critical Care and CardiologySaiseikai Kumamoto HospitalKumamotoJapan

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